Henochschonlein purpura childrens hospital of philadelphia. When the blood vessels bleed, you get a rash called purpura. Case report open access a case of henoch schonlein purpura associated with scrub typhus jae hyoung im1, suk jin choi2, moonhyun chung3, seung yun lee4, young kyoung park5, hea yoon kwon1, ji hyeon baek1 and jinsoo lee1 abstract background. Schonleinhenoch purpura, anaphylactoid purpura rhumatoid purpura diagnosis diagnosis of hsp is established when at least 2 of the following 4 criteria are present. It is one of a family of conditions called vasculitis. Henochschonlein purpura is a systemic vasculitis mediated by ig a, clinically. Henochschonlein purpura hsp is a rare disease that causes the blood vessels in your skin to become irritated and swollen. It gets its name from two german doctors, johann schonlein and eduard henoch, who. She has torpid evolution, and gastrointestinal and renal complications. Henoch schonlein purpura hsp may be caused by several allergens. Symptoms of this disease include skin lesions, joint pain, blood in urine hematuria, and abdominal pain. Apr 09, 2012 this feature is not available right now. Henochschonlein purpura hsp with kidney involvement overview this infokid topic is for parents and carers about childrens kidney conditions.
Henochschonlein purpura, who presented to our department with cutaneous manifestations. The names of some the various types of vasculitis are. Henochschonlein purpura hsp is an immune mechanism leukocytoclastic vasculitis with small vessel involvement. Henoch schonlein purpura, who presented to our department with cutaneous manifestations. Henoch schonlein purpura is caused by an abnormal immune system response in which the bodys immune system attacks the bodys own cells and organs. Henoch schonlein purpura is a small vessel vasculitis that affects mainly pediatric patients, characterized by the tetrad of palpable purpura, abdominal pain, arthralgia or arthritis. Henochschonlein purpura national kidney federation.
Henoch schonlein purpura hsp, also called immunoglobulin a vasculitis igav, is a vascular disease that primarily affects small blood vessels. Henoch schonlein purpura also known as anaphylactoid purpura is a type of vasculitis that affects small blood vessels and characterized by elevated immunoglobulin a iga. Henochschonlein purpura anaphylactoid purpura, vascular purpura internal medicine an acquired form of small vessel vasculitis with igadominant immune deposits affecting small vesselsarteries, capillaries, venules, typically of the skin, gut, and glomeruli, associated with arthralgia andor arthritis. Hsp is a condition where there is inflammation of blood vessels. It is characterized by a triad of palpable purpura without thrombocytopenia, abdominal pain.
Hsp is usually selflimiting in 94% of children and 89% of adults. It is characterized by palpable purpura, arthritis, abdominal pain and renal involvement. Henoch schonlein purpura hsp is a type of vasculitis, which means inflammation of the blood vessels. Hsp can affect blood vessels in the bowel and the kidneys, as well.
Health professionals diagnosis henoch schonlein purpura through blood tests elevated iga. The classic symptom of hsp is a red to dark purple rash, called purpura, which is often most severe on the legs and buttocks. Jul 26, 2017 henochschonlein purpura hsp is a disease that causes small blood vessels to become inflamed and leak blood. Henochschonlein purpura is a small vessel vasculitis that affects mainly pediatric patients, characterized by the tetrad of palpable purpura, abdominal pain, arthralgia or arthritis. Purpura occur in all cases, joint pains and arthritis in 80%, and abdominal pain in 62%. Other symptoms include painful swelling around the joints and abdominal pain. Background 1st described in 1801 by william heberden, a physician in london, who wrote. Some include gastrointestinal hemorrhage as a fourth criterion.
Henochschonlein purpura is a small vessel vasculitis that affects mainly pediatric patients, characterized by the tetrad of palpable purpura, abdominal pain, arthralgia or arthritis and kidney. Henochschonlein purpura is caused by an abnormal immune system response in which the bodys immune system attacks the bodys own cells and organs. The classic symptom of hsp is a red to dark purple rash, called purpura, which is often most severe. Gastrointestinal manifestations are highly variable. It affects children, mainly males, in 90% of cases the four main clinical features include purpura rash, abdominal pain, arthralgia and renal involvement. Henochschonlein purpura hsp is the most common vasculitis in children, affecting 8 to 20 children per 100 000 annually. A case of henochschonlein purpura associated with scrub. Purpura, arthritis, and abdominal pain are known as the classic triad of henochschonlein purpura. In the presence of certain clinical features the possibility of an underlying vasculitic disease must be considered. Hsp is the most common form of vasculitis in childhood and affects about 20 in 100,000 children. Nov 16, 2018 please use one of the following formats to cite this article in your essay, paper or report.
Henochschonlein purpura hsp is a form of vasculitis, a condition that involves inflammation of the blood vessels. Please use one of the following formats to cite this article in your essay, paper or report. Box 5000, fin90014 university of oulu, finland 2005 oulu, finland abstract the aim of this work was to evaluate the outcome of childhood henochschonlein purpura hsp. Among the 12 patients with recurrent or chronic henochschonlein purpura, three had arthritis, four exhibited signs and symptoms of abdominal involvement and seven of kidney disease. Hsp is most common in younger pts clinical red maculopapules on legs and buttocks. It affects children, mainly males, in 90% of cases the four main clinical features include purpura.
411 427 1064 1608 1476 1661 1012 1428 129 901 1195 292 454 157 922 893 992 1517 390 428 259 724 724 976 864 278 806 971 1554 62 718 1202 874 1097 1013 452 442 1181 730 708 1295 1458 915 1036 1480 679 503 226 242 1081 436